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Which age group normally get Von Gierke's disease?

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Final answer:

Von Gierke's disease is typically diagnosed in infancy or early childhood due to symptoms that manifest shortly after birth.

Step-by-step explanation:

The age group that normally gets Von Gierke's disease is not specified in the provided references, so it's important to know that Von Gierke's disease, or glycogen storage disease type I, is typically diagnosed in infancy or early childhood. This is because the symptoms like prolonged neonatal jaundice tend to manifest shortly after birth. Von Gierke's disease results from a deficiency in the enzyme glucose-6-phosphatase, crucial for glycogen breakdown, affecting glucose release from the liver. In terms of inheritance, it is an autosomal recessive disorder, which means that both males and females can be affected equally, despite the initial mistaken reference to an X-linked inheritance pattern and G6PD deficiency, which is a different condition.

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