Final answer:
In cases of hemophilia, it is crucial to quickly administer clotting factor concentrate after an injury to prevent bleeding. The wife's preparation of the infusion is appropriate and should proceed under medical guidance. Regular infusions are standard care for maintaining clotting factor levels.
Step-by-step explanation:
Your patient has hemophilia, a genetic disorder characterized by deficiencies in clotting factors, which leads to a propensity for bleeding. Hemophilia A and B are linked to the X chromosome and involve deficiencies in factor VIII and IX, respectively. Hemophilia C, involving factor XI, is caused by an autosomal chromosome mutation and is not sex-linked. It is vital to administer clotting factor concentrate promptly after any injury to prevent excessive bleeding. Since the patient's wife is already preparing the infusion of the prescribed concentrate, it is essential to ensure it is administered as per the doctor's instructions to control bleeding.
Furthermore, regularly scheduled infusions can help maintain adequate clotting factor levels in the bloodstream to prevent spontaneous bleeds. While gene therapy may become an option for treating hemophilia in the future, currently, administration of clotting factor concentrates is the standard treatment to manage this condition effectively.