Question

What are the size guidelines related to pregnancy for aortic root replacement in Marfan's syndrome?

1) pre pregnancy
2) during pregnancy
3) when at highest risk of rupture
4) how often surveillance

Answer 1

The size guidelines related to aortic root replacement in Marfan's syndrome vary depending on the situation. Pre-pregnancy, the aortic root diameter should be less than 4.0 cm. During pregnancy, it should be less than 4.5 cm. Surgical intervention is typically recommended when the aortic root diameter reaches 5.0 cm or greater.

Step-by-step explanation:

The size guidelines related to aortic root replacement in Marfan's syndrome can vary depending on the situation.

Pre-pregnancy:

For women with Marfan's syndrome who are considering pregnancy, the aortic root diameter should be less than 4.0 cm before the pregnancy to reduce the risk of aortic dissection during pregnancy.

During pregnancy:

During pregnancy, the aortic root diameter should be less than 4.5 cm to minimize the risk of aortic dissection or rupture.

Highest risk of rupture:

The highest risk of aortic dissection or rupture typically occurs when the aortic root diameter reaches 5.0 cm or greater. Surgical intervention is usually recommended at this stage.

Surveillance:

Regular surveillance, such as echocardiography, is important for monitoring the aortic root diameter. The frequency of surveillance may vary depending on the individual's condition and the recommendations of their healthcare provider.