Final answer:
Peutz-Jeghers syndrome is the autosomal dominant inherited disorder characterized by intestinal hamartomatous polyps and distinct skin and mucosal pigmentation. It should not be confused with other conditions such as Neurofibromatosis type 1. Individuals with an autosomal dominant disorder have a 50 percent chance of passing it to their offspring.
Step-by-step explanation:
The autosomal dominant inherited disorder characterized by intestinal hamartomatous polyps in association with a distinct pattern of skin and mucosal macular melanin deposition is Peutz-Jeghers syndrome. This syndrome is distinct from other genetic conditions such as Neurofibromatosis type 1, which involves tumor formation within the nervous system and can also lead to skin and skeletal deformities, but does not typically involve intestinal polyps. Autosomal dominant disorders are expressed with just one copy of the gene, meaning that individuals with Peutz-Jeghers syndrome have a 50 percent chance of passing the disorder on to their offspring. Examples of other autosomal dominant conditions include achondroplastic dwarfism, Marfan syndrome, and Huntington's disease, each with their specific symptoms and effects on the body.
Learn more about Peutz-Jeghers syndrome here: