Final answer:
The question discusses Friedrich Ataxia, a neurodegenerative genetic disorder leading to HOCM and CHF as the common cause of death, and compares its inheritance pattern to that of Huntington's disease.
Step-by-step explanation:
The question refers to Friedrich Ataxia, an autosomal recessive neurodegenerative disorder characterized by poor limb coordination and muscle atrophy, which progressively leads to heart complications and death. Friedrich Ataxia is caused by trinucleotide repeat expansions within genes, leading to the production of misfolded proteins that damage nerve cells, particularly within the cerebellum, affecting movement coordination. The most common cause of death in Friedrich Ataxia is Hypertrophic Obstructive Cardiomyopathy (HOCM) leading to congestive heart failure (CHF). Similarly, Huntington's disease is another genetic disorder caused by trinucleotide repeat expansions, but unlike Friedrich Ataxia, it has an autosomal dominant inheritance pattern, where the presence of a single faulty gene can cause the disease, which typically manifests later in life.